Female form of persistent mullerian duct syndrome: rare entity
Solanki Shailesh
Gowrishankar
Jadhav, Vinay
Babu, M. Narendra
Ramesh, S.
Gowrishankar
Jadhav, Vinay
Babu, M. Narendra
Ramesh, S.
NSCB Medical College ; , Department of Surgery ;
Urology Annals Journal Country: Saudi Arabia
P-ISSN: 0974-7796 E-ISSN: 0974-7834 Type of Publication: Case Reports Category: Humans, Female, Type of Research: Clinical
Keywords: 46, XY Disorders of Sex Development / Diagnosis
Broad Subjects: Maternal, Reproductive and Child Health, Anti-Mullerian Hormone ,Cryptorchidism
Citation: Shailesh Solanki ,Gowrishankar ,Vinay Jadhav ,M. Narendra Babu ,S. Ramesh , Female form of persistent mullerian duct syndrome: rare entity, Urol. Ann. 2015; 7 (1): 104-106
Persistent Mullerian duct syndrome [PMDS] is a rare form of Disorder of sex development in which Mullerian duct derivatives [fallopian tubes, uterus and the proximal vagina] are present in an otherwise normally differentiated 46 XY male. In the majority of cases, PMDS is a surprise finding either during orchidopexy or during inguinal hernia repair. We report a case of 4 year child with female type [Type III] PMDS. We are discussing the presentation, management and review of the literature
